Sclerodactyly

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Sclerodactyly
SpecialtyDermatology Edit this on Wikidata

Sclerodactyly is a localized thickening and tightness of the skin of the

Raynaud's phenomenon when it is part of systemic scleroderma.[citation needed
]

The term "sclerodactyly" comes from the combination of the Greek words "skleros" meaning hard and "daktylos" meaning a finger or toe – "hard fingers or toes".

It is generally associated with systemic

auto-immune disorders
.

Sclerodactyly is one component of the

Huriez Syndrome, along with palmoplantar keratoderma and skin cancer.[5] Sclerodactyly sometimes arises as a complication of the microvascular changes seen in diabetes mellitus, and is in this case referred to as diabetic sclerodactyly.[6][7][8]

Treatment of sclerodactyly is by physical therapy, phototherapy, surgery, topical corticosteroids or vitamin D analogues, and systemic immunosuppressive drugs when the condition is part of systemic scleroderma[citation needed]. Localized treatment won't halt systemic disease, but can restore function and cosmetic aspects of the affected digits. The mild to moderate proximal interphalangeal (PIP) joint flexion and extension contractures and stiff distal interphalangeal (DIP) joints in slight flexion often seen in sclerodactyly can be addressed somewhat with physical therapy.[9] In a few cases when immune involvement isn't apparent (in these cases environmental causes are suspected), the condition may gradually clear up by itself If the trigger is avoided[citation needed]. In other cases, early treatment while the disease is in the inflammatory stage is much more likely to be successful than on established lesions[citation needed].

See also

References

  1. ^ "Sclerodactyly: MedlinePlus Medical Encyclopedia Image". medlineplus.gov. Retrieved 2022-08-12.
  2. ^ "Systemic sclerosis | DermNet NZ". dermnetnz.org. Retrieved 2022-08-12.
  3. ISSN 2168-6068
    .
  4. ^ "CREST syndrome: MedlinePlus Medical Encyclopedia Image". medlineplus.gov. Retrieved 2022-08-12.
  5. PMID 1613149
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  9. ^ Skirven, Terri (2021). Rehabilitation of the Hand and Upper Extremity (7th ed.). Elsevier.