Laryngeal cleft

Source: Wikipedia, the free encyclopedia.

A laryngeal cleft or laryngotracheoesophageal cleft is a rare

oesophagus and the trachea, which allows food or fluid to pass into the airway.[3]

Presentation

Associated conditions

Twenty to 27% of individuals with a laryngeal cleft also have a

Diagnosis

Laryngeal cleft is usually diagnosed in an infant after they develop problems with feeding, such as coughing,

thoracic trachea.[5] Subclassification of type IV clefts into Type IVA (extension to 5 mm below the innominate artery) and Type IV B (extension greater than 5 mm below the innominate artery) may help with preoperative selection of those who can be repaired via transtracheal approach (Type IV A) versus a cricotracheal separation approach (type IV B).[6][7]

Treatment

Treatment of a laryngeal cleft depends on the length and resulting severity of symptoms. A shallow cleft (Type I) may not require surgical intervention.[5] Symptoms may be able to be managed by thickening the infant's feeds.[5] If symptomatic, Type I clefts can be sutured closed or injected with filler as a temporary fix to determine if obliterating the cleft is beneficial and whether or not a more formal closure is required at a later date.[8] Slightly longer clefts (Type II and short Type III) can be repaired endoscopically. Short type IV clefts extending to within 5 mm below the innominate artery can be repaired through the neck by splitting the trachea vertically in the midline and suturing the back layers of the esophagus and trachea closed.[6] A long, tapered piece of rib graft can be placed between the esophageal and tracheal layers to make them rigid so the patient will not require a tracheotomy after the surgery and to decrease chances of fistula postoperatively.[6] Long Type IV clefts extending further than 5 mm below the innominate artery cannot be reached with a vertical incision in the trachea, and therefore are best repaired through cricotracheal resection.[7] This involves separating the trachea from the cricoid cartilage, leaving the patient intubated through the trachea, suturing each of the esophagus and the back wall of the trachea closed independently, and then reattaching the trachea to the cricoid cartilage.[7] This prevents the need for pulmonary bypass or extracorporeal membrane oxygenation.[citation needed]

References