Annuloaortic ectasia
Annuloaortic ectasia | |
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Other names | Cystic medial necrosis of aorta descending thoracic aorta, abdominal aorta, suprarenal abdominal aorta, and infrarenal abdominal aorta. |
Specialty | Cardiology |
Annuloaortic ectasia is characterized by pure aortic valve regurgitation and aneurysmal dilatation of the ascending aorta.[2] Men are more likely than women to develop idiopathic annuloaortic ectasia, which usually manifests in the fourth or sixth decades of life. Additional factors that contribute to this condition include osteogenesis imperfecta, inflammatory aortic diseases, intrinsic valve disease, Loeys-Dietz syndrome, Marfan syndrome, and operated congenital heart disease.[3]
On a gross level, there is a pear-shaped, symmetric enlargement due to proximal aortic dilation. The aortic wall dilatation at the commissural level causes the
The term was first coined by the American heart surgeon Denton Cooley in 1961.[4]
Signs and symptoms
Symptoms are often neurological or circulatory.
Treatment
For many years, the gold standard treatment for patients with aortic valve disease and aortic root aneurysms was to replace both the aortic valve and the ascending aorta with a composite graft. This also applies to patients with different levels of AI and annuloaortic ectasia, where the aortic valve may be largely preserved without any structural abnormalities.[10]
See also
References
- ^ "Orphanet: Familial aortic dissection". Orpha.net. Retrieved 29 May 2019.
- PMID 15590080. Retrieved December 29, 2023.
- ^ ISBN 9780124202191. Retrieved December 29, 2023.
- ISBN 9781451113150.
- PMID 15975349. Retrieved December 29, 2023.
- PMID 11948080. Retrieved December 29, 2023.
- PMID 17646055. Retrieved December 29, 2023.
- PMID 11845892. Retrieved December 29, 2023.
- PMID 31454202.
- PMID 29657952.
Further reading
- Mestres, Gaspar; Riambau, Vincent; Seidman, M.A.; McManus, B.M.; Misra, Durga Prasanna; Negi, Vir Singh; Sato, Hiroshi; Tamiya, Yukihiko; Fishbein, G.A.; Buja, L.M.; Schoen, F.J.; Butany, J. (January 1, 2016). Aneurysms of the Aorta: Ascending, Thoracic and Abdominal and Their Management. Academic Press. pp. 169–211. ISBN 9780124202191. Retrieved December 29, 2023.
- Cooley, Denton A. (1985). "Annuloaortic Ectasia: Surgical Repair Using a Composite ST. JUDE MEDICAL® Valve and DACRON® Tube Graft". Cardiac Valve Replacement. Boston, MA: Springer US. pp. 73–81. ISBN 978-1-4612-9629-4.