Clear-cell sarcoma of the kidney
Clear-cell sarcoma of the kidney | |
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Specialty | Oncology, nephrology |
Clear cell sarcoma of the kidney (CCSK) is an extremely rare type of
Despite the similarities in names, clear cell sarcoma of the kidney is unrelated to clear cell sarcoma of soft tissue, also known as malignant melanoma of soft parts.[2]
Signs and symptoms
Typical gross features include large size (mean diameter 11.3 cm), a mucoid texture, foci of necrosis, and prominent cyst formation.[3]
Cause
Research in 2005 showed that CCSK can arise within a renal mesenchymal cell that shows a wide variety of neural markers.[4] Typical presentation is between 1 and 4 years of age, and a 2:1 male-to-female ratio is observed.[5]
Treatment
2004 research showed that CCSK patients exhibit an improved relapse-free survival from a longer course of therapy when using
References
External links
- Clear cell sarcoma of the kidney entry in the public domain NCI Dictionary of Cancer Terms
This article incorporates